嘌呤核苷酸(purine nucleotides)之分解過程中,何種酵素之先天性缺陷會造成dATP 貯積,傷害免疫細胞,引起嚴重之免疫缺乏症(immunodeficiency)?
adenine phosphoribsyl transferase
xanthine oxidase
adenosine deaminase
purine nucleoside phosphorylase